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KMID : 0387820060130020233
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Clinical Pediatric Hematology-Oncology
2006 Volume.13 No. 2 p.233 ~ p.237
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A Case of Malignant Extrarenal Rhabdoid Tumor of the Neck
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Jin Hye-Young
Oh Sang-Min
Kim Sun-Young
Lee Ji-Joung
Kim Jin-Man
Park Kyung-Duk
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Abstract
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Malignant rhabdoid tumor is a rare but distinctive neoplasm of unknown histogenesis, occurring primarily in children. Extrarenal rhabdoid tumors have since been reported in multiple anatomic sites in the pediatric and adult populations. These tumors are characterized by an aggressive clinical course, resistance to treatment, and a rapidly fatal outcome. We experienced a case of malignant extrarenal rhabdoid tumor located in the posterior cervical area in a 16 month-old girl. The tumor was composed of round or polygonal monotonous cells with vesicular, prominent nucleoli and abundant cytoplasm containing inclusions. On immunohistochemistry, the atypical cells were vimentin and epithelial membrane antigen (EMA) positive. After having obtained consent, the patient was treated with systemic multiagent chemotherapy and will be receiving myeloablative chemotherapy and stem cell transplantation.
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KEYWORD
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Malignant extrarenal rhabdoid tumor, Neck
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